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nintedanibBlue Cross Blue Shield of Montana

idiopathic pulmonary fibrosis (IPF)

Initial criteria

  • Diagnosis of idiopathic pulmonary fibrosis (IPF) AND exclusion of other known causes of interstitial lung disease (e.g., environmental exposures, connective tissue disease, drug toxicity)
  • Diagnostic confirmation with high-resolution computed tomography (HRCT) or surgical lung biopsy showing usual interstitial pneumonia (UIP) or probable UIP pattern