Carbaglu — CareFirst (Caremark)
N-acetylglutamate synthase (NAGS) deficiency
Initial criteria
- The diagnosis is confirmed by enzymatic, biochemical, or genetic testing
 - The member has elevated plasma ammonia levels at baseline
 
Reauthorization criteria
- Member is experiencing benefit from therapy as evidenced by a decrease in ammonia levels from baseline
 
Approval duration
12 months