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RivflozaCareFirst (Caremark)

Primary hyperoxaluria type 1 (PH1)

Initial criteria

  • Member is age ≥ 2 years
  • Diagnosis of PH1 confirmed by molecular genetic test demonstrating a mutation in the alanine:glyoxylate aminotransferase (AGXT) gene OR liver enzyme analysis demonstrating absent or significantly reduced alanine:glyoxylate aminotransferase (AGT) activity
  • Member has relatively preserved kidney function (eGFR ≥ 30 mL/min/1.73 m2)
  • Requested medication will not be used in combination with lumasiran

Reauthorization criteria

  • Member continues to meet all initial criteria
  • Member demonstrates a positive response to therapy (e.g., decrease or normalization in urinary and/or plasma oxalate levels, improvement in kidney function)

Approval duration

12 months