Carbaglu (carglumic acid tablets for oral suspension) — Cigna
Methylmalonic acidemia with hyperammonemia (acute treatment)
Initial criteria
- Patient’s plasma ammonia level is ≥ 50 micromol/L; AND
- Medication is prescribed in conjunction with other ammonia-lowering therapies (e.g., intravenous glucose, insulin, L-carnitine, protein restriction, dialysis); AND
- Medication is prescribed by or in consultation with a metabolic disease specialist (or specialist who focuses on the treatment of metabolic diseases).
Approval duration
7 days