Adempas (riociguat) — Highmark
WHO Group 1 pulmonary arterial hypertension (PAH)
Initial criteria
- Prescribed by or in consultation with a cardiovascular or pulmonary specialist
- Diagnosis of WHO Group 1 PAH (ICD-10: I27.0, I27.21)
- Documented NYHA or WHO Functional Class II or III symptoms from baseline
- Results of right heart catheterization showing ALL of the following: mean pulmonary arterial pressure (mPAP) > 20 mmHg at rest AND pulmonary wedge pressure (PWP) ≤ 15 mmHg AND pulmonary vascular resistance (PVR) ≥ 3 Wood units