Adempas (riociguat) — Highmark
WHO Group 4 chronic thromboembolic pulmonary hypertension (CTEPH)
Initial criteria
- Prescribed by or in consultation with a cardiovascular or pulmonary specialist
 - Diagnosis of WHO Group 4 CTEPH (ICD-10: I27.24)
 - Results of right heart catheterization and V/Q scan showing ALL of the following: mean pulmonary arterial pressure (mPAP) > 20 mmHg at rest AND pulmonary wedge pressure (PWP) ≤ 15 mmHg AND documented presence of occlusive thrombi within the pulmonary arteries
 - Using Adempas for recurrent or residual pulmonary hypertension after surgery OR if disease is inoperable