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Arcalyst (rilonacept)Highmark

Deficiency of Interleukin-1 Receptor Antagonist (DIRA)

Initial criteria

  • member weighs ≥ 10 kg
  • diagnosis of DIRA requiring maintenance of remission
  • prescribed by or in consultation with a rheumatologist, geneticist, dermatologist, or physician specializing in the treatment of autoinflammatory disorders
  • genetic testing has confirmed a mutation in the IL1RN gene
  • member has previously experienced clinical benefit from Kineret (anakinra) for induction treatment of DIRA

Reauthorization criteria

  • member is tolerating therapy AND has experienced disease improvement OR delayed disease progression