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Pulmonary Arterial Hypertension (PAH) – WHO Group 1

Initial criteria

  • Documented diagnosis of pulmonary arterial hypertension (PAH) – World Health Organization (WHO) Group 1
  • Prescribed by or in consultation with a cardiologist or pulmonologist
  • Documentation diagnosis is confirmed by right heart catheterization with one (1) of the following parameters:
  • Mean pulmonary artery pressure (PAP) ≥ 25 mmHg at rest or ≥ 30 mmHg with exertion
  • Pulmonary capillary wedge pressure (PCWP) ≤ 15 mmHg
  • Pulmonary vascular resistance (PVR) > 3 Wood units