Carbaglu (carglumic acid) — United Healthcare
Hyperammonemia due to propionic acidemia (PA)
Initial criteria
- Diagnosis of hyperammonemia due to one of the following: N-acetylglutamate synthase (NAGS) deficiency OR propionic acidemia (PA) OR methylmalonic acidemia (MMA)
Reauthorization criteria
- Documentation of positive clinical response to Carbaglu therapy
Approval duration
12 months