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The Policy VaultThe Policy Vault

Cuvrior (trientine tetrahydrochloride)United Healthcare

Wilson’s disease

Initial criteria

  • Diagnosis of Wilson’s disease
  • Patient is de-coppered (serum non-ceruloplasmin copper [NCC] level ≥ 25 and ≤ 150 mcg/L)
  • Patient is tolerant to penicillamine
  • Patient will discontinue penicillamine before starting therapy with Cuvrior

Reauthorization criteria

  • Documentation of positive clinical response to Cuvrior therapy

Approval duration

12 months