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NityrUnited Healthcare

hereditary tyrosinemia type 1 (HT-1)

Initial criteria

  • Diagnosis of hereditary tyrosinemia type 1
  • Nityr is being used as an adjunct to diet modification

Reauthorization criteria

  • Patient shows evidence of positive clinical response (e.g., decrease in urinary/plasma succinylacetone and alpha-1-microglobulin levels) while on Nityr therapy

Approval duration

12 months